Jornal de Citologia e Histologia

Primary Cutaneous Mucinous Carcinoma of the Vulva Displaying a Papillary Pattern

Abstract

Aditi Ranade and Antonio Macias

Primary cutaneous mucinous carcinoma (PCMC) is an extremely rare, low grade, adnexal sweat gland neoplasm that commonly affects the head and neck in the elderly population. Microscopically, it typically shows islands of epithelial cells floating in pools of mucin separated by fibrous septae. Recurrence after excision is common but metastasis is rare. Cutaneous mucinous carcinoma of the vulva is an extremely rare tumor. We report here one such case in an 89 year-old female which on histology revealed a multicystic tumor with tumor cells arranged in the form of papillae, floating in pools of mucin within the cysts. Our case thus illustrates an uncommon histological pattern of vulvar PCMC and discusses its clinical significance.