Jornal de relatos de casos clínicos

Exceptional Triad of Pulmonary Hemangioma, Rapid Involuting Congenital Hemangioma (RICH) and Atrial Septal Defect (ASD): A Case Report

Abstract

Ghaleb S, Sutton L, Milligan T and Durham L

Background: Congenital hemangiomas are rare vascular tumors of infancy classified as rapidly involuting congenital hemangiomas (RICH) and non-involuting congenital hemangiomas. Intrathoracic hemangiomas are extremely rare and pulmonary hemangiomas specifically, are exceptional and usually solitary lesions.

Case presentation: We present in this report the special case of a newborn with a triad of a congenital pulmonary hemangioma, cutaneous RICH and an atrial septal defect (ASD).

Conclusion: This is, to our knowledge, a first case of a triad of congenital pulmonary hemangioma, along with cutaneous RICH and an ASD that can be particularly important in clinical management given that the volume overload associated with an ASD, when added to the lung pathology of pulmonary hemangiomas, can lead long-term to possible pulmonary hypertension.